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Full-Text Articles in Medicine and Health Sciences
Juvenile Muscular Amyotrophy Of Distal Upper Limbs: A Casereport, Tzu-Ying Sung, Shu-Fen Sun, Po-Chin Wang, Chiao-Wen Hwang, Jue-Long Wang
Juvenile Muscular Amyotrophy Of Distal Upper Limbs: A Casereport, Tzu-Ying Sung, Shu-Fen Sun, Po-Chin Wang, Chiao-Wen Hwang, Jue-Long Wang
Rehabilitation Practice and Science
Juvenile muscular amyotrophy of distal upper limbs (Hirayama disease) is a rare disease predominantly affecting the anterior horn cells of the cervical cord in young men. It is a kind of cervical myelopathy characterized by insidious onset of unilateral distal dominant upper limbs muscle weakness and atrophy due to anterior cervical cord compression. It is difficult to differentiate this disease from other diseases with similar symptoms such as motor neuron disease. Cervical magnetic resonance (MR) study in flexed position is helpful to confirm the diagnosis.We reported a 21-year-old man who complained of slowly progressed muscle atrophy and weakness of right …
Clinical Diagnosis And Prognosis Of Hirayama Disease: A Casereport, Min-Jung Wu, Jan-Wei Chiu, Chen-Liang Chou, Rai-Chi Chan
Clinical Diagnosis And Prognosis Of Hirayama Disease: A Casereport, Min-Jung Wu, Jan-Wei Chiu, Chen-Liang Chou, Rai-Chi Chan
Rehabilitation Practice and Science
Hirayama disease is a rare disease with unique clinical manifestations. It was first reported by Japanese physician Keizo Hirayama, and tends to develop in young people in their teens and early twenties, predominantly in men. The lower cervical spinal anterior horn cells are usually involved, resulting in asymmetric muscular atrophy or weakness of distal upper extremity. The onset is insidious and gradual. It ends up in a stable status after years of progression. By now the mechanism is still unclear, and two hypotheses are discussed. One is anterior displacement of the cervical dural sac from repeated or sustained neck flexion, …